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《MPA》课件.ppt


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Classification
Diagrammaticrepresentationofthetypicalvascularsitesinvolvedwiththemorecommonformsofvasculitis,aswellasth
Classification
Diagrammaticrepresentationofthetypicalvascularsitesinvolvedwiththemorecommonformsofvasculitis,.
PrimaryVasculitides
PredominantlyLargeVesselVasculitides
Takayasu‘sarteritis
Giantcellarteritis(temporalarteritis)
Cogan'ssyndrome
Behçet'sdisease
PredominantlyMediumVesselVasculitides
Polyarteritisnodosa
Cutaneouspolyarteritisnodosa
Buerger'sdisease
Kawasakidisease(MCLS)
Primaryangiitisofthecentralnervoussystem
PredominantlySmallVesselVasculitides
Goodpasture'sdisease(anti–glomerularbasementmembranedisease)
IdiopathicCutaneousVasculitis
(Cutaneousleukocytoclasticangiitis,hypersensitivityvasculitis)
Henoch-Schönleinpurpura
Hypocomplementemicurticarialvasculitis
Essentialcryoglobulinemia
Erythemaelevatumdiutinum
ANCA-associateddisorders
Wegener‘sgranulomatosis
Microscopicpolyangiitis
Churg-Strausssyndrome
Renal-limitedvasculitis
SecondaryFormsofVasculitis
MiscellaneousSmallVesselVasculitides
Connectivetissuedisorders(rheumatoidvasculitis,lupuserythematosus,Sjögren'ssyndrome,inflammatorymyopathies)
Inflammatoryboweldisease
Paraneoplastic
Infection
Drug-inducedvasculitis:ANCA-associated,other
Pathogenicimmunecomplexformationand/ordeposition
  Henoch-Schönleinpurpura
  Vasculitisassociatedwithcollagenvasculardiseases
  Serumsicknessandcutaneousvasculitissyndromes
  HepatitisC–associatedessentialmixedcryoglobulinemia
  HepatitisB–associatedpolyarteritisnodosa
Productionofantineutrophiliccytoplasmicantibodies
ANCA:antineutrophiliccytoplasmicantibodies
  Wegener'sgranulomatosis
  Churg-Strausssyndrome
  Microscopicpolyangiitis
AECA:anti-endothelialcellAbs
PathogenicTlymphocyteresponsesandgranulomaformation
  Giantcellarteritis
  Takayasu'sarteritis
  Wegener'sgranulomatosis
  Churg-Strausssyndrome
PotentialMechanismsofVasculitisSyndromes
显微镜下多血管炎
Microscop

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  • 时间2022-09-14